An Update on the Molecular Genetics of Congenital Adrenal Hyperplasia: Diagnostic and Therapeutic Aspects

A. Wedell, Stockholm, Sweden ............ 581

ORIGINAL CONTRIBUTIONS

Pattern of Presentation of the Human Growth Hormone Variant (hGH-V) Gene in the Normal Population

J.A. Costoya, V. Arce and J. Devesa, Santiago de Compostela, Spain ............... 591

Functional Adrenal Cortical Tumors in Childhood: A Study of Ploidy, p53-Protein and Nucleolar Organizer Regions (AgNORs) as Prognostic Markers

M. Venara, R. Sanchez Marull, I. Bergada, M. Gamboni and H. Chemes, Buenos Aires, Argentina ............ 597

Possible Role of Plasma Neurotensin on Growth Hormone Regulation in Neonates

M. Bozzola, A. Ntodou-Thome, G. Bona, M. Autelli, M.L. Magnani, G. Radetti and R.-M. Schimpff, Pavia, Novara and Bolzano, Italy and Paris, France ............ 607

Plasma Neurotensin Levels in Prepubertal Children and Adults: Possible Involvement in the Regulation of Growth Hormone Secretion

M. Bozzola, A. Ntodou Thome, E. Giraldi, A.-M. Lhiaubet and R.-M. Schimpff, Pavia, Italy and Paris, France ........... 615

Clinical and Molecular Characterization of a Brazilian Patient with Pit-1 Deficiency

I.J.P. Arnhold, M. Nery, M.R. Brown, T.C. Voss, T.C. VanderHeyden, M.E. Addess, D.L. Hurley, B.L. Wajchenberg and J.S. Parks, São Paulo, Brazil and Atlanta, GA, and New Orleans, LA, USA ........... 623

Clinical Evaluation in Isolated Hypogonadotrophic Hypogonadism (Kallmann Syndrome)

P. Dissaneevate, G.L. Warne and M.R. Zacharin, Parkville, Australia ........... 631

Normal Values of Overnight Albumin Excretion Rate in a Sample of Healthy Italian Children and Adolescents

R. Lorini, G. d’Annunzio, L. Vitali, A. Scaramuzza, L. Bacchella and L.A. Zonta, Pavia, Italy .......... 639

Plasma Somatostatin and Cholecystokinin Levels in Preterm Infants During Kangaroo Care With and Without Nasogastric Tube-feeding

C.-J. Törnhage, F. Serenius, K. Uvnäs-Moberg and T. Lindberg, Umeå, Uppsala and Stockholm, Sweden .......... 645

Serum Leptin in Obese Patients with Laron Syndrome Before and During IGF-I Treatment

Z. Laron, A. Silbergeld, P. Lilos and F.W.F. Blum, Tel Aviv, Israel and Germany ............ 653

PATIENT REPORTS

Female Pseudohermaphroditism Associated with a Novel Homozygous G-to-A (V370-to-M) Substitution in the P-450 Aromatase Gene

M. Ludwig, A. Beck, L. Wickert, U. Bolkenius, B. Tittel, K. Hinkel and F. Bidlingmaier, Bonn and Dresden, Germany ........ 657

Pituitary Macroadenoma and Cushing’s Disease in Pediatric Patients: Patient Report and Review of the Literature

D. Damiani, C.H. Aguiar, C.E. Crivellaro, J.A. Galvão, V. Dichtchekenian and N. Setian, São Paulo, Brazil ........... 665

BOOK REVIEWS ........ 671

FORUM AND CORRESPONDENCE ......... 674