JOURNAL OF PEDIATRIC ENDOCRINOLOGY & METABOLISM
VOLUME
11, SUPPLEMENT 3, DECEMBER, 1998
CONTENTS
L. Ruggiero and V. de Sanctis, Italy
........... 773
Bone Pain In Thalassaemia: Assessment of DEXA and
MRI Findings
M. Angastiniotis, N. Pavlides, K. Aristidou, A.
Kanakas, M. Yerakaris, E. Eracleous and Th. Posporis, Cyprus
........... 779
Bone Density and Metabolism in Thalassaemia
R. Lala, P. Chiabotto, M. Di Stefano, G. C. Isaia,
F. Garofalo and A. Piga, Italy ............. 785
pQCT (Quantitative Peripheral Tomography) and Data
Evaluation of Phosphocalcic Metabolism in Thalassaemic Patients
B. Bagni, G. Palazzi, I. Bagni, C. Caporali, W.
Froehlich, A. Casolo, C. Caputo, S. Rossi, E. Garetti, F. Pansini, T.
Corazzari, V. De Sanctis and F. Massolo, Italy ................ 791
Genetic and Acquired Predisposing Factors and
Treatment of Osteoporosis in Thalassaemia Major
B. Wonke, C. Jensen, J.J. Hanslip, E. Prescott, M.
Lalloz, M. Layton, S. Erten, S. Tuck, J.E. Agnew, K. Raja, K. Davies and A.V.
Hoffbrand, UK ............ 795
The Diagnosis of Childhood Growth Hormone
Insufficiency and Growth Hormone Resistance
S.A. McGrath and P.M.G. Bouloux, UK ............
803
Short Stature and Body Proportion in Thalassaemia
M. Caruso-Nicoletti, V. De Sanctis, M. Capra, G.
Cardinale, L.Cuccia, F. Di Gregorio, A. Filosa, M.C. Galati, A. Lauriola, R.
Malizia, A. Mangiagli, F. Massolo, C. Mastrangelo, A. Meo, M.F. Messina1, G.
Ponzi, G. Raiola, L. Ruggiero, G. Tamborino and A. Saviano, Italy .........
811
Long Term Follow-up of Skeletal Dysplasia in
Thalassaemia Major
A. Naselli, M. Vignolo, E. Di Battista, P. Garzia,
G.L. Forni, T. Traverso and G. Aicardi, Italy ............. 817
Growth Hormone Secretion and Bone Histomorphometric
Study in Thalassaemic Patients with Acquired Skeletal Dysplasia Secondary to
Desferrioxamine
V. De Sanctis, S. Stea, L. Savarino, V. Scialpi,
G.C. Traina, G.M. Chiarelli, M. Sprocati, R. Govoni, D. Pezzoli, R. Gamberini
and F. Rigolin, Italy ............ 827
Growth and Management of Short Stature in
Thalassaemia Major
C. Theodoridis, V. Ladis, A. Papatheodorou, H.
Berdousi, F. Palamidou, C. Evagelopoulou, K. Athanassaki, O. Konstantoura and
C. Kattamis, Greece ............ 835
Short-Term Therapy with Recombinant Growth Hormone
in Polytransfused Thalassaemia Major Patients with Growth Deficiency
L. Cavallo, R. Gurrado, C. Zecchino, F. Manolo, V.
De Sanctis, M. Cisternino, M. Caruso Nicoletti and M. Galati, Italy .........
845
Acute Metabolic Effects of Human Growth Hormone on 15N-Nitrogen
Balance in Patients with Thalassaemia as Compared to
Patients with Other Types of Short Stature
Milo Zachmann, Bianca Kempken and Vincenzo De
Sanctis, Switzerland and Italy ............. 851
New GH Secretagogues and Potential Usefulness in
Thalassemia
I. Karydis, A. Tolis and G. Tolis, Greece and
Canada ........... 857
Glucose Tolerance, Insulin Secretion and Peripheral
Sensitivity in Thalassaemia Major
T. Arrigo, G. Crisafulli, A. Meo, M. Sturiale, F.
Lombardo, M. Miceli, D. Cucinotta and F. De Luca, Italy ........... 863
Epidemiology and Chelation Therapy Effects on
Glucose Homeostasis in Thalassaemic Patients
M.R. Gamberini, M. Fortini, G. Gilli, M.R. Testa and
V. De Sanctis, Italy ........... 867
Glucose Disturbances and Regulation with
Glibenclamide in Thalassemia
V. Ladis, C. Theodorides, F. Palamidou, S.
Frissiras, H. Berdousi and C. Kattamis, Greece .......... 871
Prevalence of Retinopathy in Diabetic Thalassaemic
Patients
C. Incorvaia, F. Parmeggiani, G. Mingrone, A.
Sebastiani and V. De Sanctis, Italy ............. 879
Hormonal Replacement Therapy with HCG and HU-FSH in
Thalassaemic Patients Affected by Hypogonadotropic Hypogonadism
M. Cisternino, S. Magni Manzoni, E. Coslovich and M.
Autelli, Italy ............. 885
Clinical Experience Using the Androderm®
Testosterone Transdermal System in Hypogonadal Adolescents and Young Men with b-Thalassemia
Major
V. De Sanctis, C. Vullo, L. Urso, F. Rigolin, A.
Cavallini, K. Caramelli, C. Daugherty and N. Mazer, Italy and USA ............
891
Transfusional Transmitted Viruses in Pregnancy
A. Eleftheriou, G. Kalakoutis and N. Pavlides, Cyprus
............ 901
Thrombotic Risk In Thalassemic Patients
S. Moratelli, V. De Sanctis, D. Gemmati, M.L.
Serino, R. Mari, M.R. Gamberini and G.L. Scapoli, Italy ............ 915
Pregnancy Management and Outcomes in Women with
Thalassaemia Major
S.M. Tuck, C.E. Jensen, B. Wonke and A. Yardumian, UK
............... 923
Preliminary Observations about Assisted Reproduction
in Thalassaemia
P. Negri, V. De Sanctis, E. Grechi, M.R. Gamberini
and L. Urso, Italy ............... 929
Fertility in Female Patients with Thalassemia
N. Skordis, S. Christou, M. Koliou, N. Pavlides and
M. Angastiniotis, Cyprus ................... 935
Fertility in Thalassemia: The Greek Experience
M. Karagiorga-Lagana, Greece ............. 945
POSTERS
Glucose Intolerance in Patients with Thalassemia
Major: Insulin Resistance and Hyperproinsulinemia
H. Cario, R.W. Holl and E. Kohne, Germany
........... 953
Growth Failure and Bone Lesions due to
Desferrioxamine in Thalassaemic Patients
M. Caruso-Nicoletti, D. Di Bella, G. Pizzarelli, C.
Leonardi, C. Sciuto, M. Coco and F. Di Gregorio, Italy .............. 957
Evaluation of Spine and Hip Bone Density by DXA and
QCT in Thalassemic Patients
L. Danesi, R. Cherubini, L. Ciceri, G. Graziadei,
M.D. Cappellini, F. Cavagnini and S. Ortolani, Italy ............. 961
Bone Density Study of Thalassemic Patients from
Reggio Calabria Province
D.G. D’Ascola, M.
Caminiti, G. Pagano Mariano, C. Giuffrè, S. Parlongo, P. Meduri and M. Brugiatelli, Italy ............... 963
Final Height and Endocrine Function in Thalassaemia
Intermedia
V. De Sanctis, A. Tangerini, M.R. Testa, A.L.
Lauriola, M.R. Gamberini, A.R. Cavallini and F. Rigolin, Italy
............. 965
b-Cell
Secretion in Thalassemia Major Patients
E. Ferrari, A. Bergomi, G. Palazzi, S. Rossi, S.
Forese and F. Massolo, Italy ................973
High Incidence of Osteoporosis in Thalassaemia Major
C.E. Jensen, S.M. Tuck, J.E. Agnew, S. Koneru, R.W.
Morris, A. Yardumian, E. Prescott, A.V. Hoffbrand and B. Wonke, UK ...........
975
Rachitic Rosary in a Well Chelated Thalassaemic
Patient with Primary Amenorrhea (Patient Report)
A.L. Lauriola, A. Tangerini, A. Lodi, M.R.
Gamberini, M.R. Testa, C. Orzincolo, V. De Sanctis and C. Vullo, Italy
.............. 979
Zinc Deficiency and Cell-Mediated and Humoral Autoimmunity
of Insulin-Dependent Diabetes in Thalassemic Subjects
R. Malizia, A. Scorsone, P. D’Angelo, C. Lo Pinto,
L. Pitrolo and C. Giordano, Italy .............. 981
Glucose Tolerance and b-Cell
Secretion in Patients with Thalassaemia Major
A. Mangiagli, S. Italia and S. Campisi, Italy
............. 985
Induction of Ovulation in Thalassemic Patients
C. Pafumi, L. Ciotta, G. Pernicone, M.A. Palumbo, F.
Di Gregorio, M. Caruso-Nicoletti, M. Conversano, A. Cianci and G. Palumbo, Italy
..........987
Osteopenia in Female b-Thalassemic Patients
C. Pafumi, L. Roccasalva, G. Pernicone, G. Spanò,
M.A. Palumbo, F. Di Gregorio, M. Caruso-Nicoletti, M. Conversano, A. Cianci and
G. Palumbo, Italy ........... 989
Screening for Beta-Thalassemia Heterozygotes in Pregnant
Women
C. Pafumi, A. Moschetto, G. Pernicone, M.A. Palumbo,
L. Chinnici, A. Cianci and G. Palumbo, Italy ........... 993
Human Chorionic Gonadotrophin Therapy in Hypogonadal
Thalassaemic Patients with Osteopenia: Increase in Bone Mineral Density
R. Perniola, C. De Rinaldis and M. Muratore, Italy
............ 995
Pituitary Deficiency and Lack of Gonads in an XY
Pseudohermaphrodite with b39/Lepore Haemoglobinopathy
A. Saviano, A. Filosa, D. Pasquali, M. Lamba, M.C.
Siciliani, M.M. Rinaldi, A. Bellastella, and A.A. Sinisi, Italy
.............. 997
An Endocrinologist’s Commentary
R. Stanhope, UK ............ 1001
Indexes.............. 1003
©Freund Publishing
House Ltd. 1998
ISSN 0334-018X/11-S3
232 pages
PRICE: $55.00